Severe cutaneous thrombosis with hemorrhagic necrosis in a patient with paroxysmal nocturnal hemoglobinuria: A case report and review of literature

Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, chronic acquired clonal stem cell disorder, typically manifesting hemolysis, pancytopenia and thrombosis in various organs. PNH-associated cutaneous thrombosis is extremely rare. Herein, we report a case of severe cutaneous thrombosis with hemorrh...

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Bibliographic Details
Main Authors: Fu-Nien Hsieh, Tsai-Yun Chen, Julia Yu-Yun Lee
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2017-09-01
Series:Dermatologica Sinica
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S1027811716300957