Erdheim-Chester Disease: Case Report with Aggressive Multisystem Manifestations and Review of the Literature
Erdheim-Chester disease (ECD) is an extremely rare and aggressive form of non-Langerhans cell histiocytosis. ECD usually presents with bone pain in adults aged 40–60. Its etiology is unknown but it is thought to be either a reactive or neoplastic disorder. Recently, mutation of the proto-oncogene BR...
Main Authors: | , , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Karger Publishers
2017-06-01
|
Series: | Case Reports in Oncology |
Subjects: | |
Online Access: | http://prod.karger.com/Article/FullText/477336 |