Impaired functional exercise capacity and greater cardiovascular response to the 6-min walk test in congenital generalized lipodystrophy

Abstract Background Congenital Generalized Lipodystrophy (CGL) is an ultra-rare disease characterized by metabolic disorders. However, the evaluation of functional exercise capacity, cardiovascular (CV) response to exercise, and peripheral arterial disease (PAD) in CGL is scarce. Here we evaluated t...

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Main Authors: Jorge Luiz Dantas de Medeiros, Bruno Carneiro Bezerra, Helen Rainara Araújo Cruz, Katarina Azevedo de Medeiros, Maria Eduarda Cardoso de Melo, Aquiles Sales Craveiro Sarmento, Marcela Abbott Galvão Ururahy, Lucymara Fassarella Agnez Lima, Alcebíades José dos Santos Neto, Josivan Gomes Lima, Vanessa Resqueti, Lucien Peroni Gualdi, Guilherme Fregonezi, Julliane Tamara Araújo de Melo Campos
Format: Article
Language:English
Published: BMC 2022-08-01
Series:BMC Cardiovascular Disorders
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Online Access:https://doi.org/10.1186/s12872-022-02828-x