Lung Inflammation in STING-Associated Vasculopathy with Onset in Infancy (SAVI)
STING-associated vasculopathy with onset in infancy (SAVI) is a type I interferonopathy caused by gain-of-function mutations in <i>STING1</i> encoding stimulator of interferon genes (STING) protein. SAVI is characterized by severe inflammatory lung disease, a feature not observed in prev...
Main Authors: | , |
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Format: | Article |
Language: | English |
Published: |
MDPI AG
2022-01-01
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Series: | Cells |
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Online Access: | https://www.mdpi.com/2073-4409/11/3/318 |