Pathophysiology of Hip Disorders in Patients with Mucopolysaccharidosis IVA

Pathophysiology of Hip Disorders in Patients with Mucopolysaccharidosis IVA

Patients with mucopolysaccharidoses IVA (MPS IVA) have a progressive accumulation of the specific glycosaminoglycans (GAGs): chondroitin-6-sulfate (C6S) and keratan sulfate (KS), leading to the degeneration of the cartilage matrix and its connective tissue perturbing the regular microarchitecture of...

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Bibliographic Details
Main Authors: Zhigang Wang, Yunlan Xu, Enze Jiang, Jianmin Wang, Shunji Tomatsu, Kaiying Shen
Format: Article
Language:English
Published: MDPI AG 2020-04-01
Series:Diagnostics
Subjects:
mucopolysaccharidosis IVA
femoral head osteonecrosis
hip dysplasia
cartilaginous characteristics
magnetic resonance imaging
Online Access:https://www.mdpi.com/2075-4418/10/5/264

Internet

https://www.mdpi.com/2075-4418/10/5/264

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