Significance of autoimmune disease in severe pulmonary hypertension complicating extensive pulmonary fibrosis: a prospective cohort study

The association of autoimmune disease (AI) with transplant-free survival in the setting of severe Group 3 pulmonary hypertension and extensive pulmonary fibrosis remains unclear. We report cases of severe pulmonary hypertension (mean pulmonary artery pressure ≥35 mmHg and right ventricular dysfuncti...

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Bibliographic Details
Main Authors: Rajeev Saggar, Paresh C. Giri, Chunqin Deng, Dana Johnson, Mary K. McCloy, Lloyd Liang, Faisal Shaikh, Jason Hong, Richard N. Channick, Shelley S. Shapiro, Joseph P. Lynch, John A. Belperio, Samuel S. Weigt, Allison L. Ramsey, David J. Ross, David M. Sayah, Michael Y. Shino, Ariss Derhovanessian, Alexander E. Sherman, Rajan Saggar
Format: Article
Language:English
Published: Wiley 2021-04-01
Series:Pulmonary Circulation
Online Access:https://doi.org/10.1177/20458940211011329