Marfan Syndrome beyond Aortic Root—Phenotyping Using Cardiovascular Magnetic Resonance Imaging and Clinical Implications

Marfan syndrome (MFS) is an inherited autosomal-dominant connective tissue disorder with multiorgan involvement including musculoskeletal, respiratory, cardiovascular, ocular, and skin manifestations. Life expectancy in patients with MFS is primarily determined by the degree of cardiovascular involv...

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Bibliographic Details
Main Authors: Evangelia Nyktari, Maria Drakopoulou, Panagiotis Rozos, Sofia Loukopoulou, Thomas Vrachliotis, Soultana Kourtidou, Konstantinos Toutouzas
Format: Article
Language:English
Published: MDPI AG 2023-05-01
Series:Medicina
Subjects:
Online Access:https://www.mdpi.com/1648-9144/59/5/942