Marfan Syndrome beyond Aortic Root—Phenotyping Using Cardiovascular Magnetic Resonance Imaging and Clinical Implications

Marfan syndrome (MFS) is an inherited autosomal-dominant connective tissue disorder with multiorgan involvement including musculoskeletal, respiratory, cardiovascular, ocular, and skin manifestations. Life expectancy in patients with MFS is primarily determined by the degree of cardiovascular involv...

ver descrição completa

Detalhes bibliográficos
Main Authors: Evangelia Nyktari, Maria Drakopoulou, Panagiotis Rozos, Sofia Loukopoulou, Thomas Vrachliotis, Soultana Kourtidou, Konstantinos Toutouzas
Formato: Artigo
Idioma:English
Publicado em: MDPI AG 2023-05-01
Colecção:Medicina
Assuntos:
Acesso em linha:https://www.mdpi.com/1648-9144/59/5/942