The Challenge of Diagnosing and Managing Pulmonary Arterial Hypertension in Systemic Sclerosis with Interstitial Lung Disease

Pulmonary hypertension (PH) in patients with Systemic Sclerosis (SSc) may stem from a variety of underlying causes, thus making a correct diagnosis and management difficult. The main challenges lie in the distinction between pulmonary arterial hypertension (PAH, group 1) and PH due to interstitial l...

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Bibliographic Details
Main Authors: Elisabetta Zanatta, Martina Perazzolo Marra, Giulia Famoso, Elisabetta Balestro, Chiara Giraudo, Fiorella Calabrese, Federico Rea, Andrea Doria
Format: Article
Language:English
Published: MDPI AG 2022-08-01
Series:Pharmaceuticals
Subjects:
Online Access:https://www.mdpi.com/1424-8247/15/9/1042