Real-world data of thrombotic microangiopathy management: The key role of ADAMTS13 activity and complement testing

ADAMTS13 (A Disintegrin and Metalloprotease with ThromboSpondin type 1 motifs) activity is a key tool in differential diagnosis of thrombotic microangiopathies (TMAs). Due to the lack of availability of ADAMTS13 testing, PLASMIC/PLASIC scores have been suggested to predict ADAMTS13 deficiency. The i...

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Main Authors: Eleni Gavriilaki, Eudoxia-Evaggelia Koravou, Thomas Chatziconstantinou, Christina Kalpadaki, Nikoleta Printza, Maria Ximeri, Anna Christoforidou, George Karavalakis, Maria Kaliou, Vassiliki Kalaitzidou, Iliana Tassi, Maria Tzellou, Tasoula Touloumenidou, Apostolia Papalexandri, Maria Papathanasiou, Antonia Syrigou, Anna Kioumi, Maria Liga, Georgia Kaiafa, Alexandros Spyridonidis, Eleni Kapsali, Konstantinos Kollios, Eudokia Mandala, Efthymia Vlachaki, Panagiotis Tsirigotis, Eleni Papadaki, Chrysavgi Lalayanni, Ioanna Sakellari, Achilles Anagnostopoulos
Format: Article
Language:English
Published: Elsevier 2021-05-01
Series:Thrombosis Update
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Online Access:http://www.sciencedirect.com/science/article/pii/S2666572721000122