Assessing thrombogenesis and treatment response in congenital thrombotic thrombocytopenic purpura

Assessing thrombogenesis and treatment response in congenital thrombotic thrombocytopenic purpura

Abstract Despite clinical remission and normal platelet counts, congenital TTP (cTTP) is associated with non‐overt symptoms. Prophylactic ADAMTS13 replacement therapy such as plasma infusion (PI) prevents acute episodes and improves symptomatology. There is no current method to investigate disease s...

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Bibliographic Details
Main Authors: Ferras Alwan, Chiara Vendramin, Ulrich Budde, Ri Liesner, Alice Taylor, Mari Thomas, Bernhard Lämmle, Marie Scully
Format: Article
Language:English
Published: Wiley 2021-05-01
Series:eJHaem
Subjects:
congenital TTP
prophylaxis
shear flow
upshaw schulman syndrome
Online Access:https://doi.org/10.1002/jha2.178

Internet

https://doi.org/10.1002/jha2.178

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