Impairment of respiratory muscle strength in Berardinelli-Seip congenital lipodystrophy subjects

Impairment of respiratory muscle strength in Berardinelli-Seip congenital lipodystrophy subjects

Abstract Background Berardinelli-Seip Congenital Generalized Lipodystrophy (BSCL) is an ultra-rare metabolic disease characterized by hypertriglyceridemia, hyperinsulinemia, hyperglycemia, hypoleptinemia, and diabetes mellitus. Although cardiovascular disturbances have been observed in BSCL patients...

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Bibliographic Details
Main Authors: Jorge Luiz Dantas de Medeiros, Bruno Carneiro Bezerra, Thiago Anderson Brito de Araújo, Aquiles Sales Craveiro Sarmento, Lázaro Batista de Azevedo Medeiros, Lucien Peroni Gualdi, Maria do Socorro Luna Cruz, Thaiza Teixeira Xavier Nobre, Josivan Gomes Lima, Julliane Tamara Araújo de Melo Campos
Format: Article
Language:English
Published: BMC 2018-09-01
Series:Respiratory Research
Subjects:
Lipodystrophy
MIP
MEP
PMS
Metreleptin
Online Access:http://link.springer.com/article/10.1186/s12931-018-0879-8

Internet

http://link.springer.com/article/10.1186/s12931-018-0879-8

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