Mitochondria in Huntington’s disease: implications in pathogenesis and mitochondrial-targeted therapeutic strategies
Huntington’s disease is a genetic disease caused by expanded CAG repeats on exon 1 of the huntingtin gene located on chromosome 4. Compelling evidence implicates impaired mitochondrial energetics, altered mitochondrial biogenesis and quality control, disturbed mitochondrial trafficking, oxidative st...
Main Authors: | Anamaria Jurcau, Carolina Maria Jurcau |
---|---|
Format: | Article |
Language: | English |
Published: |
Wolters Kluwer Medknow Publications
2023-01-01
|
Series: | Neural Regeneration Research |
Subjects: | |
Online Access: | http://www.nrronline.org/article.asp?issn=1673-5374;year=2023;volume=18;issue=7;spage=1472;epage=1477;aulast=Jurcau |
Similar Items
-
Time-Course of Redox Status, Redox-Related, and Mitochondrial-Dynamics-Related Gene Expression after an Acute Bout of Different Physical Exercise Protocols
by: Ramon Alves Pires, et al.
Published: (2022-12-01) -
A Pacific Oyster-Derived Antioxidant, DHMBA, Protects Renal Tubular HK-2 Cells against Oxidative Stress via Reduction of Mitochondrial ROS Production and Fragmentation
by: Hsin-Jung Ho, et al.
Published: (2023-06-01) -
Mitochondrial quality control and its role in osteoporosis
by: Chunlu Yan, et al.
Published: (2023-01-01) -
Mitochondrial stress response and myogenic differentiation
by: Fu Lin, et al.
Published: (2024-04-01) -
Mitochondrial Dysfunction in Individuals with Diabetic Kidney Disease: A Systematic Review
by: Nicole Flemming, et al.
Published: (2022-08-01)