Arrhythmogenesis in Fabry Disease
<p><strong>Purpose of Review</p></strong> Fabry Disease (FD) is a rare lysosomal storage disorder characterised by multiorgan accumulation of glycosphingolipid due to deficiency in the enzyme α-galactosidase A. Cardiac sphingolipid accumulation triggers various types of arr...
Päätekijät: | , , , , , , , |
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Aineistotyyppi: | Journal article |
Kieli: | English |
Julkaistu: |
Springer Nature
2024
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