(1)H NMR-linked metabolomics analysis of liver from a mouse model of NP-C1 disease

Clinical manifestations of Niemann-Pick type C1 (NP-C1) disease include neonatal hepatosplenomegaly and in some patients progressive liver dysfunction and failure. This study involved a (1)H NMR-linked metabolomics analysis of liver samples collected from a NP-C1 disease mutant mouse model in order...

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Bibliographic Details
Main Authors: Ruiz-Rodado, V, Nicoli, E, Probert, F, Smith, D, Morris, L, Wassif, C, Platt, F, Grootveld, M
Format: Journal article
Language:English
Published: American Chemical Society 2016