Peutz-Jeghers syndrome.
Peutz-Jeghers syndrome (PJS, MIM 175,2000) is a disease of autosomal dominant inheritance that is characterised by hamartomatous gastrointestinal polyps and mucocutaneous pigmentation. In addition to problems such as intussusception, PJS predisposes to cancers of several sites. The unusual combinati...
Main Authors: | , |
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Format: | Journal article |
Language: | English |
Published: |
1997
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