Mutations in the human muscle LIM protein gene in families with hypertrophic cardiomyopathy.

Mutations in the human muscle LIM protein gene in families with hypertrophic cardiomyopathy.

BACKGROUND: Muscle LIM protein (MLP) is an essential nuclear regulator of myogenic differentiation. Additionally, it may act as an integrator of protein assembly of the actin-based cytoskeleton. MLP-knockout mice develop a marked cardiac hypertrophy reaction and dilated cardiomyopathy (DCM). MLP is...

पूर्ण विवरण

ग्रंथसूची विवरण
मुख्य लेखकों:	Geier, C, Perrot, A, Ozcelik, C, Binner, P, Counsell, D, Hoffmann, K, Pilz, B, Martiniak, Y, Gehmlich, K, van der Ven, P, Fürst, DO, Vornwald, A, von Hodenberg, E, Nürnberg, P, Scheffold, T, Dietz, R, Osterziel, K
स्वरूप:	Journal article
भाषा:	English
प्रकाशित:	2003

समान संसाधन

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Metabolomics in hypertrophic cardiomyopathy and other myocardial diseases
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Changes in the cardiac metabolome caused by perhexiline treatment in a mouse model of hypertrophic cardiomyopathy.
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Distinct subgroups in hypertrophic cardiomyopathy in the NHLBI HCM registry
द्वारा: Neubauer, S, और अन्य
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Effects of propranolol on response to exercise in hypertrophic obstructive cardiomyopathy.
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द्वारा: Watkins, H, और अन्य
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