Molecular studies of stiff skin-causing mutations in fibrillin-1

Molecular studies of stiff skin-causing mutations in fibrillin-1

<p>Fibrillin-1 is the main component of the 10-12 nm microfibrils, which are found in several elastic and non-elastic tissues. Human fibrillin-1 contains multiple calcium-binding epidermal growth factor-like (cbEGF) domains interspersed with transforming growth factor β-binding protein-like (T...

書誌詳細
第一著者:	Iqbal, S
その他の著者:	Handford, P
フォーマット:	学位論文
言語:	English
出版事項:	2011
主題:	Biochemistry Biology

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