Phenotypic and molecular heterogeneity in fibrodysplasia ossificans progressiva.

Fibrodysplasia (myositis) ossificans progressiva (FOP) is an extremely rare inherited disorder in which progressive ossification of major striated muscles, often following injury, is associated with abnormal skeletal patterning. Altered expression of bone morphogenetic proteins may be a contributory...

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Autors principals: Virdi, A, Shore, E, Oreffo, R, Li, M, Connor, J, Smith, R, Kaplan, F, Triffitt, J
Format: Journal article
Idioma:English
Publicat: 1999