Alternative splicing of dystrobrevin regulates the stoichiometry of syntrophin binding to the dystrophin protein complex.

Alternative splicing of dystrobrevin regulates the stoichiometry of syntrophin binding to the dystrophin protein complex.

Dystrophin coordinates the assembly of a complex of structural and signalling proteins that is required for normal muscle function. A key component of the dystrophin-associated protein complex (DPC) is alpha-dystrobrevin, a dystrophin-related and -associated protein whose absence results in muscular...

書誌詳細
主要な著者:	Newey, S, Benson, M, Ponting, C, Davies, K, Blake, D
フォーマット:	Journal article
言語:	English
出版事項:	2000

類似資料

Role of beta-dystrobrevin in nonmuscle dystrophin-associated protein complex-like complexes in kidney and liver.
著者:: Loh, N, 等
出版事項: (2001)

Assembly of multiple dystrobrevin-containing complexes in the kidney.
著者:: Loh, N, 等
出版事項: (2000)

Function and genetics of dystrophin and dystrophin-related proteins in muscle.
著者:: Blake, D, 等
出版事項: (2002)

Dysbindin, a novel coiled-coil-containing protein that interacts with the dystrobrevins in muscle and brain.
著者:: Benson, M, 等
出版事項: (2001)

Syncoilin, a novel member of the intermediate filament superfamily that interacts with alpha-dystrobrevin in skeletal muscle.
著者:: Newey, S, 等
出版事項: (2001)

Association of syncoilin and desmin: linking intermediate filament proteins to the dystrophin-associated protein complex.
著者:: Poon, E, 等
出版事項: (2002)

Delivery of AAV2/9-microdystrophin genes incorporating helix 1 of the coiled-coil motif in the C-terminal domain of dystrophin improves muscle pathology and restores the level of α1-syntrophin and α-dystrobrevin in skeletal muscles of mdx mice.
著者:: Koo, T, 等
出版事項: (2011)

Association of syncollin and desmin: Linking intermediate filament proteins to the dystrophin-associated protein complex.
著者:: Poon, E, 等
出版事項: (2002)

Dystrobrevin deficiency at the sarcolemma of patients with muscular dystrophy.
著者:: Metzinger, L, 等
出版事項: (1997)

Antagonistic regulation of alpha-actinin alternative splicing by CELF proteins and polypyrimidine tract binding protein.
著者:: Gromak, N, 等
出版事項: (2003)

Stoichiometry of a regulatory splicing complex revealed by single-molecule analyses.
著者:: Cherny, D, 等
出版事項: (2010)

A novel mechanism for modulating synaptic gene expression: differential localization of alpha-dystrobrevin transcripts in skeletal muscle.
著者:: Newey, S, 等
出版事項: (2001)

Dystrophin-associated protein complex: clinical implications.
著者:: Hilton-Jones, D, 等
出版事項: (1993)

Regulation of alternative splicing of CD45 by antagonistic effects of SR protein splicing factors.
著者:: ten Dam, G, 等
出版事項: (2000)

Protein aggregation mediates stoichiometry of protein complexes in aneuploid cells
著者:: Brennan, Christopher M, 等
出版事項: (2020)

Regulation of mRNA abundance by polypyrimidine tract-binding protein-controlled alternate 5′ splice site choice
著者:: Hamid, Fursham M., 等
出版事項: (2014)

Aneuploidy reveals insights into control of protein complex stoichiometry
著者:: Brennan, Christopher M.
出版事項: (2020)

Stoichiometry and turnover in single, functioning membrane protein complexes.
著者:: Leake, M, 等
出版事項: (2006)

Stoichiometry and turnover in single, functioning membrane protein complexes
著者:: Leake, M, 等
出版事項: (2006)

SRRM2 organizes splicing condensates to regulate alternative splicing
著者:: Xu, Shaohai, 等
出版事項: (2023)

Quantifying binding affinities, kinetics and stoichiometry of biomolecular complexes with mass photometry
著者:: Soltermann, F, 等
出版事項: (2020)

Expression of four alternative dystrophin transcripts in brain regions regulated by different promoters.
著者:: Górecki, D, 等
出版事項: (1992)

Regulation of alternative splicing in the rat fibronectin gene
著者:: Huh, Gene Simon
出版事項: (2005)

Characterization of the regulation of CD46 alternative splicing
著者:: Tang, Sze Jing
出版事項: (2016)

The PTB interacting protein raver1 regulates alpha-tropomyosin alternative splicing.
著者:: Gromak, N, 等
出版事項: (2003)

Alternative splicing regulates Prdm1/Blimp-1 DNA binding activities and corepressor interactions.
著者:: Morgan, M, 等
出版事項: (2012)

Dystrophin and utrophin are functionally homologous actin binding proteins but act through distinct modes of filament association
著者:: Rybakova, I, 等
出版事項: (2001)

Dose-Dependent Regulation of Alternative Splicing by MBNL Proteins Reveals Biomarkers for Myotonic Dystrophy
著者:: Wagner, Stacey D., 等
出版事項: (2017)

Global regulation of alternative splicing during myogenic differentiation
著者:: Bland, Christopher S., 等
出版事項: (2011)

Characterization of the regulation of CD46 RNA alternative splicing
著者:: Tang, Sze Jing, 等
出版事項: (2018)

Characterization of the alternative splicing regulating the proapoptotic gene BIM.
著者:: Lee, Qing Feng.
出版事項: (2012)

Stoichiometry /
著者:: 192544 Bhatt, Bharat I., 等
出版事項: (2004)

Stoichiometry /
著者:: 192544 Bhatt, Bharat I., 等
出版事項: (2010)

ZZ domain is essentially required for the physiological binding of dystrophin and utrophin to beta-dystroglycan.
著者:: Ishikawa-Sakurai, M, 等
出版事項: (2004)

Alternative splicing and disease /
著者:: Jeanteur, Ph. (Philippe)
出版事項: (2006)

A mechanism underlying position-specific regulation of alternative splicing
著者:: Hamid, Fursham M., 等
出版事項: (2018)

β2-Syntrophin Is a Cdk5 Substrate That Restrains the Motility of Insulin Secretory Granules
著者:: Schubert, S, 等
出版事項: (2010)

β2-syntrophin is a Cdk5 substrate that restrains the motility of insulin secretory granules
著者:: Schubert, S, 等
出版事項: (2010)

The utrophin and dystrophin genes share similarities in genomic structure.
著者:: Pearce, M, 等
出版事項: (1993)

Triple trans-splicing adeno-associated virus vectors capable of transferring the coding sequence for full-length dystrophin protein into dystrophic mice.
著者:: Koo, T, 等
出版事項: (2014)