Regular long-term red blood cell transfusions for managing chronic chest complications in sickle cell disease

<p><strong>BACKGROUND:</strong> Sickle cell disease is a genetic haemoglobin disorder, which can cause severe pain, significant end-organ damage, pulmonary complications, and premature death. Sickle cell disease is one of the most common severe monogenic disorders in the world, due...

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Autori principali: Estcourt, L, Hopewell, S, Trivella, M, Hambleton, I, Cho, G
Natura: Journal article
Lingua:English
Pubblicazione: Cochrane Collaboration 2019