New developments in treating glycosphingolipid storage diseases.

New developments in treating glycosphingolipid storage diseases.

Номзүйн дэлгэрэнгүй
Үндсэн зохиолчид:	Platt, F, Jeyakumar, M, Andersson, U, Dwek, R, Butters, T
Формат:	Journal article
Хэл сонгох:	English
Хэвлэсэн:	2005

Ижил төстэй зүйлс

Glycosphingolipid lysosomal storage diseases: therapy and pathogenesis.
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New therapeutics for the treatment of glycosphingolipid lysosomal storage diseases.
-н: Butters, T, зэрэг
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Inhibition of glycosphingolipid biosynthesis: application to lysosomal storage disorders.
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Substrate deprivation: a new therapeutic approach for the glycosphingolipid lysosomal storage diseases.
-н: Platt, F, зэрэг
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N-butyldeoxygalactonojirimycin: a more selective inhibitor of glycosphingolipid biosynthesis than N-butyldeoxynojirimycin, in vitro and in vivo.
-н: Andersson, U, зэрэг
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Lysosomal storage of oligosaccharide and glycosphingolipid in imino sugar treated cells.
-н: Boomkamp, S, зэрэг
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Storage solutions: treating lysosomal disorders of the brain.
-н: Jeyakumar, M, зэрэг
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Pharmacological impairment of acrosome formation and sperm head morphogenesis reveals essential role of glycosphingolipids in spermiogenesis
-н: van der Spoel, A, зэрэг
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Glycosphingolipid profiling of tissues from mouse models of human lysosomal storage disorders
-н: Priestman, D, зэрэг
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Impaired selection of invariant natural killer T cells in diverse mouse models of glycosphingolipid lysosomal storage diseases
-н: Silk, J, зэрэг
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Impaired selection of invariant natural killer T cells in diverse mouse models of glycosphingolipid lysosomal storage diseases.
-н: Gadola, S, зэрэг
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Cellular effects of deoxynojirimycin analogues: uptake, retention and inhibition of glycosphingolipid biosynthesis.
-н: Mellor, H, зэрэг
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Modulation of THP-1 macrophage and cholesterol-loaded foam cell apolipoprotein E levels by glycosphingolipids.
-н: Garner, B, зэрэг
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Substrate reduction therapy for glycosphingolipid storage disorders.
-н: Lachmann, R, зэрэг
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Molecular requirements of imino sugars for the selective control of N-linked glycosylation and glycosphingolipid biosynthesis
-н: Butters, T, зэрэг
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ALTERED AUTOPHAGY AND APP METABOLISM IN GLYCOSPHINGOLIPID STORAGE DISEASES
-н: Boland, B, зэрэг
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Glycosphingolipid disorders of the brain.
-н: Boomkamp, S, зэрэг
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Substrate reduction therapy in mouse models of the glycosphingolipidoses.
-н: Platt, F, зэрэг
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Introduction: Glycosphingolipids in cell biology and disease.
-н: Sillence, D, зэрэг
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Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease.
-н: Andersson, U, зэрэг
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Analysis of fluorescently labeled glycosphingolipid-derived oligosaccharides following ceramide glycanase digestion and anthranilic acid labeling.
-н: Neville, D, зэрэг
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Therapeutic applications of imino sugars in lysosomal storage disorders.
-н: Butters, T, зэрэг
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Iminosugar inhibitors for treating the lysosomal glycosphingolipidoses
-н: Butters, T, зэрэг
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Accumulation of glycosphingolipids in Niemann-Pick C disease disrupts endosomal transport.
-н: te Vruchte, D, зэрэг
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Imino sugar inhibitors for treating the lysosomal glycosphingolipidoses.
-н: Butters, T, зэрэг
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Glycosphingolipid storage leads to the enhanced degradation of the B cell receptor in Sandhoff disease mice.
-н: te Vruchte, D, зэрэг
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Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice.
-н: Garner, B, зэрэг
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Glycosphingolipids in endocytic membrane transport.
-н: Sillence, D, зэрэг
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Diverse endogenous antigens for mouse NKT cells: self-antigens that are not glycosphingolipids.
-н: Pei, B, зэрэг
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The apo E gene knockout mouse as a model to study the potential atherogenic properties of glycosphingolipids
-н: Garner, B, зэрэг
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Apoptotic modification of glycosphingolipids of human granulocytes
-н: A. M. Tomin, зэрэг
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The development and use of small molecule inhibitors of glycosphingolipid metabolism for lysosomal storage diseases
-н: James A. Shayman, зэрэг
Хэвлэсэн: (2014-07-01)

Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice
-н: Brett Garner, зэрэг
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Glycosphingolipid metabolism and its role in ageing and Parkinson’s disease
-н: Wallom, K-L, зэрэг
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Inhibition of substrate synthesis as a strategy for glycolipid lysosomal storage disease therapy.
-н: Platt, F, зэрэг
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Inhibition of glycogen breakdown by imino sugars in vitro and in vivo.
-н: Andersson, U, зэрэг
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Small-molecule therapeutics for the treatment of glycolipid lysosomal storage disorders.
-н: Butters, T, зэрэг
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Activation state and intracellular trafficking contribute to the repertoire of endogenous glycosphingolipids presented by CD1d [corrected].
-н: Muindi, K, зэрэг
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Glycosphingolipid synthesis inhibition limits osteoclast activation and myeloma bone disease
-н: Ersek, A, зэрэг
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Iminosugars and methods of treating viral diseases
-н: Ramstedt, U, зэрэг
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