New developments in treating glycosphingolipid storage diseases.

New developments in treating glycosphingolipid storage diseases.

Bibliografische gegevens
Hoofdauteurs:	Platt, F, Jeyakumar, M, Andersson, U, Dwek, R, Butters, T
Formaat:	Journal article
Taal:	English
Gepubliceerd in:	2005

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New therapeutics for the treatment of glycosphingolipid lysosomal storage diseases.
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Substrate deprivation: a new therapeutic approach for the glycosphingolipid lysosomal storage diseases.
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N-butyldeoxygalactonojirimycin: a more selective inhibitor of glycosphingolipid biosynthesis than N-butyldeoxynojirimycin, in vitro and in vivo.
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Lysosomal storage of oligosaccharide and glycosphingolipid in imino sugar treated cells.
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Storage solutions: treating lysosomal disorders of the brain.
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Impaired selection of invariant natural killer T cells in diverse mouse models of glycosphingolipid lysosomal storage diseases
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Impaired selection of invariant natural killer T cells in diverse mouse models of glycosphingolipid lysosomal storage diseases.
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Cellular effects of deoxynojirimycin analogues: uptake, retention and inhibition of glycosphingolipid biosynthesis.
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Modulation of THP-1 macrophage and cholesterol-loaded foam cell apolipoprotein E levels by glycosphingolipids.
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Substrate reduction therapy for glycosphingolipid storage disorders.
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Molecular requirements of imino sugars for the selective control of N-linked glycosylation and glycosphingolipid biosynthesis
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ALTERED AUTOPHAGY AND APP METABOLISM IN GLYCOSPHINGOLIPID STORAGE DISEASES
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Glycosphingolipid disorders of the brain.
door: Boomkamp, S, et al.
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Substrate reduction therapy in mouse models of the glycosphingolipidoses.
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Introduction: Glycosphingolipids in cell biology and disease.
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Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease.
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Analysis of fluorescently labeled glycosphingolipid-derived oligosaccharides following ceramide glycanase digestion and anthranilic acid labeling.
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Therapeutic applications of imino sugars in lysosomal storage disorders.
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Iminosugar inhibitors for treating the lysosomal glycosphingolipidoses
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Accumulation of glycosphingolipids in Niemann-Pick C disease disrupts endosomal transport.
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Imino sugar inhibitors for treating the lysosomal glycosphingolipidoses.
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Glycosphingolipid storage leads to the enhanced degradation of the B cell receptor in Sandhoff disease mice.
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Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice.
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Glycosphingolipids in endocytic membrane transport.
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Diverse endogenous antigens for mouse NKT cells: self-antigens that are not glycosphingolipids.
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The apo E gene knockout mouse as a model to study the potential atherogenic properties of glycosphingolipids
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Apoptotic modification of glycosphingolipids of human granulocytes
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The development and use of small molecule inhibitors of glycosphingolipid metabolism for lysosomal storage diseases
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Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice
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Glycosphingolipid metabolism and its role in ageing and Parkinson’s disease
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Inhibition of substrate synthesis as a strategy for glycolipid lysosomal storage disease therapy.
door: Platt, F, et al.
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Inhibition of glycogen breakdown by imino sugars in vitro and in vivo.
door: Andersson, U, et al.
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Small-molecule therapeutics for the treatment of glycolipid lysosomal storage disorders.
door: Butters, T, et al.
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Activation state and intracellular trafficking contribute to the repertoire of endogenous glycosphingolipids presented by CD1d [corrected].
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Glycosphingolipid synthesis inhibition limits osteoclast activation and myeloma bone disease
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Iminosugars and methods of treating viral diseases
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