Síndrome de Prune Belly com fístula vesicocutânea: relato de caso raro e revisão da literatura

Prune Belly syndrome (PBS) is a rare complex malformation that preferentially affects male newborns. It presents with a wide spectrum of alterations that include abdominal muscle deficiency, varying degrees of renal dysplasia and urinary tract obstruction, in addition to bilateral cryptorchidism. In...

وصف كامل

التفاصيل البيبلوغرافية
المؤلفون الرئيسيون: Debora Leticia Silva Gouvêa Viana, Naara Rafaela Gonçalves, Álvaro Henrique Anghietti Nalon, Michel Correia Viana, Rúbia Cecília Barbone e Melo, Ítalo Guilherme Giarola de Freitas Mariano, Raquel Ida Ferreira, Thais Silva Maia, Paula Silva Maia
التنسيق: مقال
اللغة:English
منشور في: Sociedade Brasileira de Pediatria 2023-12-01
سلاسل:Residência Pediátrica
الموضوعات:
الوصول للمادة أونلاين:https://cdn.publisher.gn1.link/residenciapediatrica.com.br/pdf/v13n4e696.pdf